CYSTIC PULMONARY HAMARTOMA MANIFESTING AS SPONTANEOUS PNEUMOTHORAX

Pleurectomy for spontaneous pneumothorax in cystic fibrosis.

Five cases of cystic fibrosis complicated by eight pneumothoraces are described. These cases come from a group of 49 patients who have attended the Brompton Hospital between 1964 and 1969 for management of their cystic fibrosis. Three of the patients, who had a total of six pneumothoraces, were managed by pleurectomy. Spontaneous pneumothoraces were a terminal event in a fourth patient, and an ...

Cystic Pulmonary Chondroid Hamartoma: A Case Report

composed of varying proportions of mesenchymal tissues including cartilage, fat, epithelial, and connective tissue combined with entrapped respiratory epithelium (1). Pulmonary hamartomas are the most common benign neoplasms of the lung, accounting for 7-14% of benign solitary pulmonary nodules (1, 2). Pulmonary hamartomas are most commonly presented as incidental lung nodules found on a routin...

Spontaneous pneumothorax as a first sign of pulmonary carcinoma

We report five cases of spontaneous pneumothorax as the first sign of pulmonary carcinoma. Initial tests did not detect neoplasms. Diagnosis took place during surgery for four patients and the fifth was diagnosed by preoperative computed tomography to assess pulmonary bullous emphysema. All five patients had persistent air leaks in spite of correct placement and functioning of drains, the reaso...

Spontaneous pneumothorax as a presenting pulmonary manifestation of early sarcoidosis.

Birt-Hogg-Dubé Syndrome Manifesting as Spontaneous Pneumothorax: A Novel Mutation of the Folliculin Gene

Birt-Hogg-Dubé syndrome (BHDS) is a rare disease with autosomal dominant inheritance that manifests through skin tumors, pulmonary cystic lesions, and renal tumors. A mutation of FLCN located on chromosome 17p11.2, which encodes a tumor-suppressor protein (folliculin), is responsible for the development of BHDS. We report the case of a patient presenting with spontaneous pneumothorax, in whom a...